Volume 8, Issue 9

In The Clinic: CFTR Modification & Nutritional Deficiencies

Editor's note:

If you’re interested in other valuable CF medical education, our CF Virtual Roundtable webcast is now available on-demand! Start the activity here: virtual.dkbmed.com

In this program, Peter Mogayzel, Jr., MD, PhD leads a case-based discussion with Patrick Flume, MD and Lisa Saiman, MD on challenges in treating lung infections. Watch as they cover the following topics:

Management of patients with declining FEV1

Treatment options

Reinforcing adherence

Working on inhaler techniques

Changing inhaled antibiotics

Considering a continuous, cycled, or intermittent therapy approach

Interactive monograph also available!

In this issue:

The effects of CFTR modifiers on improving lung function in people with cystic fibrosis are well known. But what about their effects on the GI tract that directly affect nutrition?

In this issue, Dr. Michael Wilschanski — Director of Hadassah Hospital’s Pediatric Gastroenterology Unit at Hebrew University in Jerusalem — explains how new findings about CFTR modification can impact clinical practice.

Learning objectives:

Describe the findings that explain the cause of weight gain in patients with CF taking ivacaftor.

Explain how exocrine pancreatic functions may be improved with ivacaftor treatment.