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TY - JOUR
T1 - Neonatal dilated cardiomyopathy
JO - Revista Portuguesa de Cardiologia (English edition)
T2 -
AU - Soares,Paulo
AU - Rocha,Gustavo
AU - Pissarra,Susana
AU - Soares,Henrique
AU - Flôr-de-Lima,Filipa
AU - Costa,Sandra
AU - Moura,Cláudia
AU - Dória,Sofia
AU - Guimarães,Hercília
SN - 08702551
M3 - 10.1016/j.repc.2016.10.007
DO - 10.1016/j.repc.2016.10.007
UR -
AB - Cardiomyopathies are rare diseases of the heart muscle, of multiple causes, that manifest with various structural and functional phenotypes but are invariably associated with cardiac dysfunction. Dilated cardiomyopathy is the commonest cardiomyopathy in children, and the majority present before one year of age. Its etiology may be acquired or genetic. Myocarditis is an important cause and is responsible for the majority of acquired cases. Inherited (familial) forms of dilated cardiomyopathy may occur in 25-50% of patients. Echocardiographic and tissue Doppler studies are the basis for diagnosis of dilated cardiomyopathy in most patients. Marked dilatation of the left ventricle with global hypokinesis is the hallmark of the disease. This review will cover the classification, epidemiology and management of newborns with dilated cardiomyopathy. In particular, a comprehensive and up-to-date review of the genetic study of dilated cardiomyopathy and of detailed echocardiographic assessment of these patients will be presented.
ER