In 1924, primary fibrosarcoma of the skin was distinguished as an entity and separated from other tumors because of its characteristic clinical and histological manifestations by Darier and Ferrand.1 It is best known as dermatofibrosarcoma protuberans. Binkley2 found that this neoplasm was first presented by Sherwell to the New York Dermatological Society in 1890, and Costa3 states that Taylor also reported a case later in 1890. Many names have been given by different authors4 to this neoplasm of the skin. The terminology of some authors suggested a benign tumor, while that of others indicated a malignant tumor. Woringer5 and Senear4d and his associates called this tumor benign, while Eller,6 Binkley,2 and others believed it to be more serious.

Over 200 cases have been recorded, including 38 cases that Pack7 recently reported. Hoffman4b was of the opinion that general surgeons excised