CONT… :

PATIENT EDUCATION :

PATIENT EDUCATION ADVICE PATIENT THAT MONTHLY VIT B12 ADMINISTRATION SHOULD BE CONTINUED FOR LIFE. TEACH THE PATIENT TO SELECT BALANCED DIET . ENCOURAGE PATIENT TO FOLLOW UP PERIODICALLY TO MONITOR CBC.

CONT…:

CONT…:

CONT… GIVE METICULOUS CARE TO OPEN WOUND IF ANY . BARRIER NURSING .

PATIENT EDUCATION :

PATIENT EDUCATION GENETIC COUNSELING TO THE FAMILY . INSTRUCT FAMILY HOW TO RECOGNISE THE SIGNS OF DEHYDRATION . ENCOURAGE GOOD DENTAL HYGEINE . INSTRUCT ON PREVENTIVE CARE INCLUDING CHILDHOOD IMMUNIZATION & SCREENING TESTS .

CONT…:

CONT… TREAT HEMARTHROSIS OR MUSCLE BLEED IMMOBILIZE THE JOINT IN A POSITION OF SLIGHT FLEXION ELEVATE THE AFFECTED PART ABOVE THE LEVEL OF HEART APPLY ICE PACKS ADMINISTER SHORT COURSE OF CORTICOSTERIODS AS ORDERED TO RELIEVE INFLAMMATION

CONT…:

CONT… 4. ACUTE PAIN R/T BLEEDING INTO THE JOINT & MUSCLES GOAL: RELIEVING PAIN NSG INTERVENTIONS BE AWARE THAT INCREASED PAIN USUALLY MEANS THAT BLEEDING CONTINUES ADMINISTER OR TEACH ADMINISTERATION OF ACETAMINOPHEN DURING ACUTE PHASE . NSAIDS MAY BE USED FOR CHRONIC PAIN