CHILDHOOD OCCIPITAL EPILEPSY (GASTAUT TYPE)

OVERVIEW

Childhood occipital epilepsy (Gastaut-type) is a
self-limiting childhood epilepsy with onset in later
childhood. Seizures are usually easily controlled and
remission of seizures occurs within 2-4 years from onset.

NOTE Self-limiting refers to
there being a high likelihood of seizures spontaneously remitting at a
predictable age.

Clinical context

This syndrome is characterized by onset of seizures between 15
months and 19 years of age (peak 8-9 years). Remission occurs in
50-60% of patients within 2-4 years after onset. A dramatic response
to carbamazepine is seen in more than 90% of patients. Both sexes are
equally affected. Antecedent and birth history is normal. Head size
and neurological examination are usually normal. Development and
cognition is normal, although mild cognitive impairment has been
described.