The congenital tuberculosis is a rare illness, difficult to be correctly diagnosed only based on the clinical manifestations and without having an available maternal history. We present the case of an autopsy of a recently born one of 56 days, a mother's of black race product, without prenatal control and of very low economic resources. The neonate presented poor suction, weak cry, hydrocephalia and little development, simulating a sepsis neonatal and necrotizant enterocolitis. The autopsy reveals tubers milliar generalized in brain, liver, spleen, pancreas, glands adrenals, thyroid, lymphatic node, kidney, heart, skeletal muscle, lung. More your mother presents a pneumonitis being isolated Mycobacterium tuberculosis.