Background: Lipoblastoma is a rare benign mesenchymal tumor of infancy and early childhood.Symptoms vary depending on localization, and signs of compression of adjacent organs may be seen.

Purpose: To determine the best surgical management of head and neck lipoblastoma in children.

Case:A 5 years old boy with painless rapid growing mass in the left temple and cheek.

Method: A structuredliterature search was performed using PubMed, EBSCO, and Cochrane, according to clinical questions.The selection of articles was based on inclusion and exclusion criteria. One selected article was assessedfor quality with criteria of critical appraisal from Oxford.

Results: Most study showed that complete tumorextirpation was the most preferred procedure in cases of child head neck lipoblastoma. In managementwith partial excision, there were some recurrence of tumor.

Conclusion: Based on the literature that hadthe highest level of evidence, complete extirpation techniques were the best choice.