The kidney changes are mostly likely found in the course of a tuberous cerebral sclerosis (Bourneville-Pringle's disease: Skin, cerebral and pulmonary changes). Sometimes also seen as a chance finding in kidney sonography (as first directing finding of a tuberous cerebral sclerosis). Very rare are kidney symptoms (i.e. Hematuria, palpable tumor).

Pathomorphology or Pathophysiology of this disease :

Composition of different parts of vessels, muscles and fat tissue. The presenting symptoms therefore vary in accordance to the composition of these tissues.

A single angiomyolipoma must not be indicative for Bourneville - Pringle's Disease.

Hyperintense in T1 and T2, due to the high fat content. Often obvious enhancement (only in ares of high vasculature). Frequently well-seen in fat-reducing sequences. CT: fat equivalent (i.e. negative HU-values in CT), occasionally however also denser representation (in higher vasculature or muscle).

Diagnosis confirmation:

Total constellation (Consens)

Which DD would be also possible with the radiological findings:

If cystic parts predominate: polycystic kidney disease

Teratoma (otherwise difficult differentials, particularly if hemorrhaging changes the picture); angiomyelofibromas do not calcify, in contrast to teratomas.Nephroblastomatosis