Hemifacial
HypertrophyHemifacial
hypertrophy may occur either isolated or associated with one of several
syndromes. Syndromes associated with facial hemihypertrophy are Proteus
syndrome, Klippel-Trenaunay-Weber syndrome, and other neurocutaneous diseases. Hemifacial hypertrophy usually
involves the cheek and is limited rostally by the orbits and caudally
by the jaw (Figure 172.1 [A]). Hemifacial hypertrophy may be accompanied
by hemimegalencephaly (Figure 172.1 [B]). Hemimegalencephaly is characterized
by hypertrophy of one cerebral hemisphere with ipsilateral ventricular
dilatation. More about...49

A

B

Figure 172.1.— Hemifacial
hypertrophy. [A] Hypertrophic tissue on the right cheek prevents the face
from moving in the direction of the hemifacial hypertrophy. [B] MRI of
the face and brain show hypertrophic facial tissue and hemimegalencephaly
on the same side.