Total Anomalous Pulmonary Venous Connection And Cor Triatriatum

Total Anomalous Pulmonary Venous Connection and Cor Triatriatum

1. Embryology

A. Total anomalous pulmonary venous connection (TAPVC) develops when the primordial pulmonary vein fails to unite with the plexus of veins surrounding the lung buds. This results in return of pulmonary venous blood to the heart via a systemic vein, and subsequently to the right atrium.