%0 Journal Article
%A Yousuf, Tariq
%A Kramer, Jason
%A Jones, Brody
%A Keshmiri, Hesam
%A Dia, Muhyaldeen
%T Pulmonary Hypertension in a Patient With Congenital Heart Defects and Heterotaxy Syndrome
%D 2016
%J Ochsner Journal
%P 309-311
%V 16
%N 3
%X Background: Heterotaxy syndrome, also called isomerism, is a condition in which abdominal and thoracic organs are located in abnormal body positions. Pulmonary hypertension (PHTN) is an uncommon clinical feature of heterotaxy syndrome.Case Report: We describe the case of a 26-year-old male who developed PHTN as a rare manifestation of heterotaxy syndrome. To our knowledge, PHTN has never been reported as a prominent clinical feature in a patient with heterotaxy syndome and congenital cardiac abnormalities.Conclusion: It is important for the clinician to be aware of potentially serious consequences of PHTN in the setting of heterotaxy syndrome.
%U http://www.ochsnerjournal.org/content/ochjnl/16/3/309.full.pdf