..PECJD has rarely been described in Caucasians and debate continues on its classification and pathogenesis. We describe our experience of PECJD over a 14-year period of surveillance for CJD in the Netherlands and the UK...

[Eleven years of autopsy on account of Creutzfeldt-Jakob disease in the Netherlands]

..To our knowledge, this is the second family worldwide in which this mutation has been identified. Gerstmann-Sträussler-Scheinker disease should be considered in patients with a clinical diagnosis of familial frontotemporal dementia...

[The first patient with the new variant of Creutzfeldt-Jakob's disease in The Netherlands]