A case of spontaneous luxation of the globe and Crouzon's disease is described. The luxation was reduced under general anaesthesia. Bilateral permanent tarsorrhaphies were performed to prevent further luxations and to decrease the lagophthalmos and corneal exposure. There was also mild bilateral optic atrophy and a left superior oblique palsy. The patient exhibited turricephaly, maxillary hypoplasia and shallow orbits with proptosis. Major reconstructive surgery is not indicated as the patient is already 9 years old and has no mental impairment.