In the prenatal ultrasound, there is evidence of foreshortened extremities (history of hip dysplasia/chondrodystrophy in the family). Prenatal ultrasound with dilated stomach, double-bubble phenonemon, oligohydramnios. Spontaneous delivery in the 37th week of pregnancy in cephalic presentation. Postnatally unremarkable adaptation. Further diagnostics.

Pathomorphology or Pathophysiology of this disease :

Internal stenoses arise more often through growth retardation than through vascular or obliterating infections. Beside membrane-like barriers, tubular strictures have been also described.

Radiological findings:

X-Ray 1: Abdominal overview, hanging. Large stomach bubble in the left upper quadrant, duodenal bubble to the right of the spine, little air in the rest of the abdomen.

X-Ray 2: UGI: Contrast media column with abrupt stop at the transition to the pars horizontalis.

Ultrasound 1: Hypoechoic structure with internal floating echos seen in the subhepatic region on the transverse abdominal view.

Ultrasound 2: Obliterating peristaltic waves traveling from the left to right.

Postnatal confirmation of the diagnosis by ultrasound and x-ray. Planned surgical repair using a duodeno-duodenostomy. Intraoperatively, a tubular stenosis was seen, which had a pinpoint sized lumen. A post-stenotic dilation was not seen. A probe could be passed through the lumen. Postoperative pain management with a peridural catheter. Quick oral nutrition through the feeding tube. The tube was removed on the 11th postoperative day and enteral nutrition was unproblematic.