Optical Coherence Tomography Findings in a Patient with Goldmann-Favre Syndrome

Mehmet Özgür ZENGİN1, Gamze MEN2, Mehmet Giray ERSÖZ3

1M.D., İzmir Tepecik Training and Research Hospital Eye Clinic, İzmir/ TURKEY2M.D. Associate Professor, İzmir Tepecik Training and Research Hospital Eye Clinic, İzmir/TURKEY3M.D. Asistant, İzmir Tepecik Training and Research Hospital Eye Clinic, İzmir/TURKEY
The aim of this study is to report the optical coherence tomography (OCT) findings in a patient diagnosed with Goldmann-Favre syndrome. A 35-year-old man complaining of visual deterioration and night blindness was evaluated. Ophthalmological examination revealed a best corrected visual acuity of 20/100 on both eyes. Fundus evaluation showed foveal microcysts (arranged like a star) along with mild atrophy of the retinal pigment epithelium. Scotopic electroretinogram (ERG) was almost non-recordable. Photopic electroretinograms showed marked reduction of the amplitudes. No leakage was observed on the fluorescein angiography. OCT revealed small cystic spaces that formed bridges between the outer and inner retinal layers in the fovea. These cystic spaces were located in all retinal layers. Collaps of the cystic spaces was observed after five-years follow-up. These findings demonstrated that OCT is a useful test to evaluate the structural findings observed in Goldmann-Favre syndrome.
Keywords :
Collaps of the cystic spaces, Goldmann-Favre syndrome, optical coherence tomography