Mucoviscidosis or Cystic Fibrosis is the most common congenital and early lethal metabolic disease in Europe. Only if diagnosed early do those affected stand a chance of living beyond young age. The following article summarizes all the facts on formation, diagnosis, therapy and prognosis of mucoviscidosis. This will prepare you comprehensively for clinical exams, practical trainings and your final exam.

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in patients presenting with major haemoptysis.
So, to summarize the discussion of airwaysdisease in this third lecture. Upper airways
obstruction is uncommon but can be life threateningand it’s often misdiagnosed as asthma or COPD.
Flow volume loops. The CT scan and bronchoscopycan identify patients with upper airways obstructions,
but you need to think about doing those tests,you need to consider those diagnosis. Bronchiectasis
is common and has multiple different causes,and the main problem is that the patients
get recurrent infections and eventually ifthey get uncontrolled recurrent infections that
will lead to progressive airways obstructionand potentially respiratory failure and death.
So controlling infections is the main aimin these patients to prevent lung function
loss over time. Cystic fibrosis is a specificcause of bronchiectasis an inherited the defect
of the CFTR gene, and that causes a very severebronchiectasis which almost invariably will
progress to severe airways obstruction butis associated with multiple other problems
such as malabsorbtion, diabetes, infertilityand obstruction. Lastly, we've discussed minor
haemoptysis which is, the main problem thereis whether the patient is maybe having lung
cancer or not. And major haemoptysis whichis a significant life threatening emergency
that requires aggressive treatment. Thank you for listening.

About the Lecture

The lecture Other Airways Diseases: Summary by Jeremy Brown, PhD is from the course Airway Diseases.

Included Quiz Questions

A patient with a mycetoma presents to hospital after coughing up 250ml of fresh blood. What should not be part of their management?

Lying the patient onto the unaffected lung

Bronchial arteriogram and embolisation

Measuring haemoglobin and clotting time

Oxygen and intravenous fluid replacement

Which of the following is the last resort or life-saving procedure when a patient has uncontrolled major hemoptysis?

Arterial embolization

Tranexamic acid

Vitamin K supplements

Nasal packing

Clotting factors

Author of lecture Other Airways Diseases: Summary

Jeremy Brown, PhD

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