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Treatment

Splenectomy to reduce thrombocytopenia has been helpful in some patients with X-linked thrombocytopenia, but it must be followed by antibiotic prophylaxis because of the increased risk of septicemia and sudden death

Platelet transfusions should be avoided unless severe bleeding has occurred

Finally, bone marrow transplantation using the best-matched donor offers the possibility of a definitive cure, but it is associated with morbidity and mortality