Figure 166

Plain radiograph of a child with prune-belly syndrome showing a markedly protuberant abdomen. This syndrome, also referred to as Eagle-Barrett syndrome or triad syndrome, occurs almost exclusively in males. The three classic physical findings are the deficiency of the abdominal wall musculature, urinary tract anomalies characterized by an extremely dilated urinary tract, and bilateral intraabdominal testes. A wide spectrum in the severity of abnormalities is seen, with most children having some degree of renal dyspla-sia, along with bladder and ureteric dys-plasias (partial or complex lack of smooth muscle). (Courtesy ofPhilip Silberberg, MD.)