Bottom Line:
Lymphomatoid granulomatosis (LyG) is a rare, angiocentric, angiodestructive, B-cell lymphoproliferative disease, presenting with pulmonary involvement in more than 80% of cases.We describe a case of primary orbital LyG in a 1-year-old child.

ABSTRACTLymphomatoid granulomatosis (LyG) is a rare, angiocentric, angiodestructive, B-cell lymphoproliferative disease, presenting with pulmonary involvement in more than 80% of cases. We describe a case of primary orbital LyG in a 1-year-old child.

Mentions:
The child's mother became concerned about a progressive swelling of the right eye over a period of weeks. There was no relevant previous medical or birth history and the mother tested negative for human immunodeficiency virus (HIV). Examination revealed gross, nonaxial proptosis associated with periorbital edema, erythema, and nasal conjunctival chemosis [Figure 1]. Ocular motility was restricted horizontally and in elevation. On fundoscopy, there was pale disc swelling on the right, with tortuous retinal vessels.

Mentions:
The child's mother became concerned about a progressive swelling of the right eye over a period of weeks. There was no relevant previous medical or birth history and the mother tested negative for human immunodeficiency virus (HIV). Examination revealed gross, nonaxial proptosis associated with periorbital edema, erythema, and nasal conjunctival chemosis [Figure 1]. Ocular motility was restricted horizontally and in elevation. On fundoscopy, there was pale disc swelling on the right, with tortuous retinal vessels.

Bottom Line:
Lymphomatoid granulomatosis (LyG) is a rare, angiocentric, angiodestructive, B-cell lymphoproliferative disease, presenting with pulmonary involvement in more than 80% of cases.We describe a case of primary orbital LyG in a 1-year-old child.

ABSTRACTLymphomatoid granulomatosis (LyG) is a rare, angiocentric, angiodestructive, B-cell lymphoproliferative disease, presenting with pulmonary involvement in more than 80% of cases. We describe a case of primary orbital LyG in a 1-year-old child.