Cervical esophageal duplication cysts occur in the upper one third of the esophagus and are the second rarest type of esophageal duplication cyst.

The location and size of the lesion determines the clinical presentation. These congenital anomalies can also be discovered as an incidental finding.

In 1711, Blasius reported the first case of esophageal duplication cyst [3]. The first reported case of a cervical esophageal duplication cyst was by Bishop and Koop in 1964. Arbona et al reviewed 50 000 autopsies and concluded that the incidence rate of these congenital anomalies was 1 in
8200.

A review of the literature documented 18 reported cases of cervical esophageal duplication cysts. Of symptomatic cases, about 50% present with respiratory distress in the first year of life.

Of the cases that reported sex, a male sex predilection (2:1) has been
observed.