Unusual presentation of posterior mediastinal chordoma in a 2-year-old boy.

MedLine Citation:

PMID:
12972813
Owner:
NLM
Status:
MEDLINE

Abstract/OtherAbstract:

Chordoma is a rare and slow-growing malignant neoplasm that arises from the embryonic notochord. It is rare to see a thoracic chordoma presenting as a posterior mediastinal mass with pleural seeding in a child. The authors report a chordoma of the thoracic spine with posterior mediastinal extension and pleural seeding in a 2-year-old boy who presented with asymmetric bilateral hand temperature and lower limb paralysis. The clinical course progressed rapidly, resulting in death.