This rare low-grade sarcoma was identified by Meis-Kindblom and Kindblom in 1998.
Patients are in their middle adult years (range third to 9th decade, median 53 years) and males and females are equally affected.
The tumor presents as a painless subcutaneous mass of months or years duration. The lesions average 3 cm in size.MRI exam will demonstrate the extent of the tumor and the regional lymph nodes and chest should be assessed.
Excision with a wide margin and long-term follow-up is required.

Adamantinoma of the long bones, or extragnathic adamantinoma, is an extremely rare, slow growing, low-grade malignant tumor of epithelial origin, that occurs almost exclusively in the tibia and the fibula.
The tumor usually occurs in the second to fifth decade of life.
The patient usually has swelling that may be painful. The duration of symptoms can vary from a few weeks to years.Adamantinoma appears as an eccentric, well-circumscribed, and lytic lesion on plain x-ray.
Adamantinoma is treated by wide surgical excision