Cardiac lipomas are very rare. We herein report a case of a 57-year-old woman who presented with intrapericardial extracavitary giant lipoma, and we also review the relevant literature. The patient had no symptoms except for a tendency to easily feel slightly fatigued. She underwent a resection of the lipoma through a clamshell thoracotomy. The lipoma weighed 1 700 g and had a cylindircal stalk measuring about 5 cm in diameter connected to the myocardium of the right ventricle.