Poland's syndrome is a rare congenital anomaly coexisting with the absence of pectoralis major and ipsilateral upper limb and chest wall deformities. Hypoplasia of the breast, agenesis of ipsilateral rib cartilage, athelia, and an ipsilateral developmental finger anomalies as syndactyly also can be seen. In the literature, only 56 patients with dextrocardia and left-sided Poland's syndrome have been described. Herein, a case of left sided Poland's syndrome coexisting with dextrocardia and nasal hemangioma was presented.